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Blistering diseases: pemphigus, bullous pemphigoid

Dermatology, Venereology and Leprosy · MBBS

Study notes

Flaccid blisters, Nikolsky positive, oral erosions — pemphigus; steroids + rituximab. Pemphigus vulgaris (flaccid blisters — oral erosions — Nikolsky positive — desmoglein: biopsy + DIF — intercellular IgG — fishnet: steroids — high-dose + rituximab — first; azathioprine — sparing): bullous pemphigoid (elderly — tense blisters — Nikolsky negative — hemidesmosome: milder — steroids — lower; doxycycline). The flaccid oral blister is pemphigus — biopsy confirms.

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